Unilateral submandibular gland aplasia with ipsilateral sublingual gland hypertrophy presenting as a neck mass.

Autores de IDIVAL

• Jaime Gallo Terán

  Autor

• Pedro Lastra García-Barón

  Autor

Autores ajenos al IDIVAL

• Herrera-Calvo G
• García-Montesinos-Perea B
• Saiz-Bustillo R

Unidades

• DIAGNÓSTICO Y TRATAMIENTO POR IMAGEN

  Investigador Responsable

  Elena Carmen Gallardo Agromayor

Abstract

The congenital absence of the major salivary glands is a very infrequent disorder, in which several glands are usually involved at the same time. Sometimes this disorder can be associated with other developmental anomalies. The unilateral aplasia of the submandibular gland is an extremely rare finding with only 14 cases reported in the literature. Clinically, this kind of patients may complain of dryness of the mouth, difficulties in chewing and swallowing, severe periodontal disease or multiple caries, but usually they follow an asymptomatic course. Salivary gland aplasia can be diagnosed with a large variety of imaging techniques, which include computer tomography (CT), magnetic resonance imaging (MR), ultrasonography (US), sialography, or scintigraphy. In this paper we report a case of a patient referred to our department with a long term and progressive growing neck mass, who has an unilateral submandibular gland aplasia associated to an ipsilateral hypertrophy of the sublingual gland.

Keywords

• Submandibular gland aplasia; sublingual gland hypertrophy; neck mass